Abstract

*Ayi T. Amah, Offiong James Aboh and Abotsi Abriba

Sickle cell (ss) diseases, a common haemoglobinopathy are an autosomal recessive disease. Hypertrophy of adenoid and tonsils have been known to persist in ss disease children than in healthy ones. Greater challenges exist during adenotonsillectomy for these patients. It is a retrospective study between January 2010 to January 2013 in University of Port Harcourt Teaching Hospital Nigeria. Case notes of (16) sixteen patients with ss disease, who had adenotonsillectomy were retrieved. Gender, Age, Various indications and challenges were recorded and analyzed. Six (6) patients presented within age range three to five years, Table 1, followed by four (4) patients presenting at age range 6 to 8 years, male/female ratio 3:2. Four (4) patients had post operative bleeding, out of which one died. Persistent low PCV were observed in almost all the patients. Challenges were enumerated in Table 4. Greater challenges are encountered in sickle cell children, undergoing adenotonsillectomy, compared to normal children.